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第45卷第2期
               ·200 ·                            南 京    医 科 大 学 学         报                        2025年2月


                         0.001  0.724  0.121  0.006  0.002  0.723  0.563  0.042  0.004  0.005  0.017  0.334  0.003  0.572  0.046  0.001  0.071  0.029  0.972  0.109  0.006
                      P                                697.10)<0.001  <0.001                                aminotransfer⁃

                                       223.00)  134.00)  135.00)  462.00)  168.00)  62.00)  994.61)         aspartate
                      (n=37)  11.47  (4.13,.39)  8  (2.85,.15)  7  (0.45,.85)  0  (0.32,.59)  0  20.10)  1  (2.42,.94)  3  (0.59,.62)  1  1  11.73)  60)  AST:


                      Death  ±  (43.24)  (134.00,  (31.00,  (45.80,  (270.00,  (33.00,  (19.50,  (3.16,  (732.62,  (746.85,  (4.24,  (0,  (35.14)  (5.41)  (8.11)  (48.65)  (2.70)  (56.76)  (18.92)  (24.32)  (83.78)  (78.38)

                         0057.70  016.00  0  006.01  0  004.96  0  000.73  0  000.50  0  171.00  0  058.80  0  069.60  0  344.00  0  074.00  0  041.50  0  008.70  0  030.75  1  003.38  0  000.95  0  278.43  006.89  0  000.32  0  013.00  0  002.00  0  003.00  0  018.00  0  001.00  0  021.00  0  007.00  0  009.00  0  031.00  0  029.00  0  aminotransferase;  glucocorticoid.




                      (n=87)  (3.82,.69)  6  (2.35,.59)  4  (0.63,.19)  1  (0.32,.60)  0  223.00)  79.70)  67.90)  346.00)  77.00)  50.25)  (2.20,.39)  7  875.25)  (2.54,.65)  3  (0.43,.25)  1  131.77)1  1  (2.57,.38)  5  alanine  ALT:  GC:  D⁃dimer;


                      Survival  13.32  ± 049.32  (37.93)  033.00  004.89  003.36  000.98  000.46  (143.00,  179.00  (24.90,  045.70  (29.20,  044.30  (247.00,  287.00  (27.00,  040.00  (22.00,  033.00  004.02  (196.53,  543.65  003.02  000.67  (445.02,  694.55  003.82  32)  (0,  000.12  (35.63)  031.00  (16.09)  014.00  (20.69)  018.00  (27.59)  024.00  (0)  000.00  (58.62)  051.00  (17.24)  015.00  (24.14)  021.00  (67.82)  059.00  (1.15)  008.00  count;  D⁃D:



                  patients  DM  P  0.030  0.451  0.561  0.277  0.003  0.844  0.023  0.337  0.005  0.012  0.113  0.773  0.001  0.001  0.220  0.099  0.014  0.003  0.980  0.014  0.370  0.044  -  <0.001  <0.001  <0.001  <0.001  platelet  PLT:  count;  fibrinogen;  FIB:



                DM患者的临床特征  anti⁃MDA5 +  of  (n=37)  RPILD  12.57  ±  (45.95)  (3.60,.39)  7  (2.84,.52)  5  (0.44,.87)  0  (0.29,.59)  0  221.00) (134.00,  126.75) (29.75,  130.75)  (38.25,  425.50) (280.00,  119.50)  (31.00,  62.00)  (21.00,  23.50)  (3.88,  636.05)  1 (738.65,  1.20  ±  (0.52,.76)  1  916.57)  1 (634.36,  10.78)  (4.06,  60)  (0,  (45.95)  (8.11)  (2.70)  (43.24)  (0)  (62.16)  (21.62)  (16.22)  (86.49)  -  (78.38)  (37.50)  (63.89)  (72.97)  monocyte absolute  serum ferri








                Anti⁃MDA5 +  characteristics  0055.73  17.00  00  5.87  000  004.21  0  000.73  0  0.47  000  168.00  0 224.00)  051.20  0  062.40  0  344.00  0 353.50)  071.00  0  036.00  0  009.15  0  977.70  0 873.60)  0003.43  01.07  000  206.81 169.00)1  006.74  0  000.08  0  017.00  0  003.00  0  001.00  0  016.00  0  000.00  0  023.00  0  008.00  0  006.00  0  032.00  0  029.00  0  012.00  0  023.00  0  027.00  0  MON:  count;  C⁃reactive  CRP:





                表1  Clinical  (n=87)  13.36  (3.89,.84)  6  (2.45,.84)  4  (0.63,.17)  1  (0.32,.60)  0  87.70)  73.15)  104.50)  51.00)  (2.22,.39)  7  (0.45,.17)  1  1  (2.72,.44)  5  32)  -  lymphocyte


                  1   Non⁃RPILD  ±  (36.78)  (148.00,  (26.10,  (30.65,  (248.00,  (27.00,  (22.00,  (227.50,  0.87  ±  (454.71,  (0,  (31.03)  (14.94)  (22.99)  (29.89)  (1.15)  (56.32)  (16.09)  (27.59)  (67.82)  (21.62)  (2.30)  (4.55)  (8.05)  absolute  sedimentation rate;
                  Table  050.16  032.00  005.06  003.58  000.98  000.47  179.00  046.80  048.60  288.00  042.00  034.00  003.96  176.03)547.20  003.15  000.67  363.50)716.83  003.92  000.16  027.00  013.00  020.00  026.00  001.00  049.00  014.00  024.00  059.00  8.00  2.00  4.00  7.00  LYC:  count;  erythrocyte




                      (n=124)  13.33  (3.85,.10)  7  (2.56,.19)  5  (0.56,.10)  1  (0.32,.60)  0  223.25)  94.97)  83.40)  389.00)  080.00)  1  51.00)  10.43)  1  (0.48,.40)  1  1  (3.03,.15)  7  40)  neutrophil  ESR:


                      Total  ±  (39.52)  (140.75,  (27.90,  (31.60,  (253.75,  (27.25,  (22.00,  (2.57,  (295.75,  0.98  ±  (478.80,  (0,  (35.48)  (12.90)  (16.94)  (33.87)  (0.81)  (58.06)  (17.74)  (24.19)  (72.58)  (29.83)  (29.83)  (11.29)  (21.77)  (27.42)  absolute  creatine kinase;
                         051.82  049.00  005.08  003.68  000.85  000.47  178.00  050.70  053.40  304.50  045.50  034.50  004.60  687.00  003.24  000.77  847.00  004.25  000.16  044.00  016.00  021.00  042.00  001.00  072.00  022.00  030.00  090.00  037.00  037.00  014.00  027.00  ]034.00


                                                                                                    ]  ]  (%)  NEU:  CK:
                             ]  ]  ]  ]  ]  ]  ]  ]  ]  ]  ]  ]  ]  ]                               (%)  [n  (%)  [n  [n  rate  count;  cell


                         s)  ]  [10 9 /L, (P25, 75)  P  M  [10 9 /L, (P25, 75)  P  M  [10 9 /L, (P25, 75)  P  M  [10 9 /L, (P25, 75)  P  M  [10 9 /L, (P25, 75)  P  M  [U/L, (P25, 75)  P  [U/L, (P25, 75)  P  [U/L, (P25, 75)  P  P  [mm/h, (P25, 75)  P  M  [mg/L, (P25, 75)  P  M  [ng/mL, (P25, 75)  P  s)  [mg/L, (P25, 75)  P  ]  ] (P25, 75)  P  P  mg/d  ]  (%)  ]  ]  rate mortality  rate mortality  mortality  blood  lactate dehydrogenase;
                         (years, ±  x  (%)  M  M  M  [U/L, (P25, 75)  M  M  (g/L, ±  x  M  (P25, 75)  P  [mg/d, (P25, 75)  M  ]  (%)  mg/d  mg/d  mg/d  mg/d  [n  (%)  [n  (%)  [n  white WBC:

                      Variable  Age  [n  Male  WBC  NEU  LYC  MON  PLT  ALT  AST  LDH  CK  ESR  CRP  SF  FIB  D⁃D  [M  SII  [M  NLR  GC  [n  GC  0  0-15  15-30  30-100  >100  Anti⁃MDA5  +++  ++  +  Anti⁃Ro52 +  RPILD  Death  3⁃month  6⁃month  12⁃month  LDH:  ase;
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